Updated International Guidelines for IPF Diagnosis: A Radiology Perspective

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Criteria for UIP Pattern

Usual interstitial pneumonia is the most common idiopathic interstitial pneumonia31 and carries the worst prognosis.30 UIP is the radiologic and pathologic pattern observed in patients with IPF,45 but UIP-like patterns are also caused by secondary conditions such as collagen vascular disease, chronic hypersensitivity pneumonitis, asbestosis, or drug toxicity,3233 highlighting the importance of identifying any possible causes of lung disease prior to diagnosing idiopathic UIP.45